C0001815 - Myeloproliferativ tilstand som utvikler seg fra en abnorm stamcelle. Den er karakterisert ved at beinmargen blir erstattet av fibrøst vev, en prosess som er utløst av cytokiner produsert i den abnorme klonen. 1/10
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293,031 терминов и синонимов из MeSH и LOINC

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Terms, descriptions
CUI    C0001815
RussianMedical Subject Headings Russian D055728 L8588892preferred S10684707 Y МИЕЛОФИБРОЗ ПЕРВИЧНЫЙ
RussianMedical Subject Headings Russian D055728 L0899235no S1103052 Y MIELOFIBROZ
RussianMedical Subject Headings Russian D055728 L0899237no S1103054 Y MIELOIDNAIA METAPLAZIIA
RussianMedical Subject Headings Russian D055728 L1519794no S1815703 Y FIBROZ KOSTNOGO MOZGA
RussianMedical Subject Headings Russian D055728 L1526985no S1822894 Y KOSTNOGO MOZGA FIBROZ
RussianMedical Subject Headings Russian D055728 L1530526no S1826435 Y MIELOSKLEROZ
RussianMedical Subject Headings Russian D055728 L1530531no S1826440 Y MIELOZ ALEIKEMICHESKII
RussianMDRRUS 10077161 L15738790no S19062945 N Первичный миелофиброз
RussianMDRRUS 10077161 L15738790no S19062945 Y Первичный миелофиброз
RussianMedical Subject Headings Russian D055728 L3353632no S3881105 Y КОСТНОГО МОЗГА ФИБРОЗ
RussianMedical Subject Headings Russian D055728 L3357674no S3885158 Y МИЕЛОЗ АЛЕЙКЕМИЧЕСКИЙ
RussianMedical Subject Headings Russian D055728 L3357683no S3885167 Y МИЕЛОИДНАЯ МЕТАПЛАЗИЯ
RussianMedical Subject Headings Russian D055728 L3357720no S3885204 Y МИЕЛОСКЛЕРОЗ
RussianMedical Subject Headings Russian D055728 L3357721no S3885205 Y МИЕЛОФИБРОЗ
RussianMedical Subject Headings Russian D055728 L3374172no S3901665 Y ФИБРОЗ КОСТНОГО МОЗГА
RussianMedical Subject Headings Russian D055728 L8587352no S10683760 Y MIELOFIBROZ PERVICHNYI
RussianMedical Subject Headings Russian D055728 L9126824no S11381008 Y IDIOPATICHESKAIA MIELOIDNAIA METAPLAZIIA
RussianMedical Subject Headings Russian D055728 L9128270no S11382073 Y ИДИОПАТИЧЕСКАЯ МИЕЛОИДНАЯ МЕТАПЛАЗИЯ
RussianMedical Subject Headings Russian D055728 L9128316no S11382391 Y ПЕРВИЧНЫЙ МИЕЛОФИБРОЗ
RussianMedical Subject Headings Russian D055728 L9128483no S11381397 Y PERVICHNYI MIELOFIBROZ
Medical Subject Headings A15581514 AT100258771 A de novo myeloproliferation arising from an abnormal stem cell. It is characterized by the replacement of bone marrow by fibrous tissue, a process that is mediated by CYTOKINES arising from the abnormal clone.
Medical Subject Headings Czech A17438592 AT204250229 Myeloproliferativní onemocnění s vazivovou přeměnou (fibrózou) kostní dřeně, myeloidní metaplazií a krvetvorbou mimo kostní dřeň (v játrech a zejm. slezině - extramedulární hemopoeza). Primární (idiopatická) m. je vzácné onemocnění s klonálním poškozením kmenové buňky neznámé etiologie. (cit. Velký lékařský slovník online, 2013 http://lekarske.slovniky.cz/ )
NCI NCI Dictionary of Cancer Terms A17693106 AT197954796 A progressive, chronic disease in which the bone marrow is replaced by fibrous tissue and blood is made in organs such as the liver and the spleen, instead of in the bone marrow. This disease is marked by an enlarged spleen and progressive anemia.
NCI Thesaurus A17693106 AT205734688 A chronic myeloproliferative neoplasm characterized by bone marrow fibrosis, proliferation of atypical megakaryocytes and granulocytes in the bone marrow, anemia, splenomegaly, and extramedullary hematopoiesis. (WHO, 2001)
MSHNOR A23541605 AT221559157 Myeloproliferativ tilstand som utvikler seg fra en abnorm stamcelle. Den er karakterisert ved at beinmargen blir erstattet av fibrøst vev, en prosess som er utløst av cytokiner produsert i den abnorme klonen.